Preduodenal Portal Vein or Malrotation

Preduodenal portal vein (PDPV) is a rare congenital anomaly and occurs either as a single malformation or in association with other malformations. PDPV is mainly asymptomatic and associated intestinal anomalies are often more likely to cause high intestinal obstruction. A neonate with recurrent bilious vomiting since birth is presented. Laparotomy revealed PDPV but it was intestinal malrotation that was causing intestinal obstruction.